Portal vein thrombosis as the first presentation of paroxysmal nocturnal hemoglobinuria

被引：1
|
作者：
Wang, Ran [1 ]
Guo, Xiaozhong [1 ]
Tang, Yufu [2 ]
Qi, Xingshun [1 ]
机构：
[1] Gen Hosp Northern Theater Command, Dept Gastroenterol, 83 Wenhua Rd, Shenyang 110840, Liaoning, Peoples R China
[2] Gen Hosp Northern Theater Command, Dept Hepatobiliary Surg, Shenyang, Peoples R China
来源：
DRUG DISCOVERIES AND THERAPEUTICS | 2022年 / 16卷 / 04期
关键词：
paroxysmal nocturnal hemoglobinuria; portal vein thrombosis; anticoagulation therapy; MANAGEMENT; RISK;
D O I：
10.5582/ddt.2022.01033
中图分类号：
R9 [药学];
学科分类号：
1007 ;
摘要：
Paroxysmal nocturnal hemoglobinuria (PNH) is a rare, acquired clonal hematopoietic stem cell disorder, characterized by hemolytic anemia, bone marrow failure and thrombosis. Portal vein thrombosis (PVT) is relatively rare in patients with PNH. In this paper, we reported PVT as the first clinical presentation of PNH in a female patient. PVT related symptoms resolved after anticoagulation therapy.
引用
收藏
页码：200 / 203
页数：4
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