[1] Louis Pradel Hosp, Natl Reference Coordinating Ctr Rare Pulm Dis, Lyon, France
[2] Hosp Civils Lyon, Lyon, France
[3] Univ Lyon, Univ Claude Bernard Lyon 1, UMR754, IVPC, F-69008 Lyon, France
[4] ERN LUNG, Lyon, France
[5] Univ Padua, Resp Dis Unit, Padua, Italy
[6] Univ Padua, Dept Cardiac Thorac Vasc Sci & Publ Hlth, Padua, Italy
[7] CHU Bourgogne, Ctr Reference Constitutif Malad Pulmonaires Rares, Serv Pneumol & Soins Intensifs Resp, Dijon, France
[8] Univ Bourgogne Franche Comte, Fac Med & Pharm, INSERM, U123 1, Dijon, France
[9] PELyon, PharmacoEpidemiol Lyon, Lyon, France
[10] F Hoffmann La Roche Ltd, Basel, Switzerland
[11] Genentech Inc, San Francisco, CA 94080 USA
[12] Univ Claude Bernard Lyon 1, Croix Rousse Univ Hosp, Resp Med, Lyon, France
[13] Univ Claude Bernard Lyon 1, EA7426, Lyon, France
[14] Univ Claude Bernard Lyon 1, Hlth Serv & Performance Res, HESPER 7425, Lyon, France