共 50 条
- [3] DRUG REPURPOSING FOR CYSTIC FIBROSIS SUBJECTS WITH RARE CFTR MUTATIONS [J]. PEDIATRIC PULMONOLOGY, 2017, 52 : S316 - S317
- [4] The cystic fibrosis transmembrane conductance regulator (CFTR) chloride channel. [J]. AMERICAN ZOOLOGIST, 2000, 40 (06): : 1046 - 1046
- [5] MOLECULAR MECHANISMS OF CFTR CHLORIDE CHANNEL DYSFUNCTION IN CYSTIC-FIBROSIS [J]. CELL, 1993, 73 (07) : 1251 - 1254
- [6] CFTR - MUTATIONS, ION-CHANNEL FUNCTION AND CYSTIC-FIBROSIS [J]. JOURNAL OF PHYSIOLOGY-LONDON, 1995, 489P : S2 - S2
- [9] Cystic Fibrosis: Channel, Catalytic, and Folding Properties of the CFTR Protein [J]. Journal of Bioenergetics and Biomembranes, 1997, 29 : 429 - 442