The incidence of congenital melanocytic nevi (CMNs) is 1% to 6% for small- to intermediate-size nevi to 1 in 500,000 for giant size nevi. Large and satellite CMNs are known to be associated with neurocutaneous melanosis and central nervous system malformations such as Dandy-Walker malformation, defects of the vertebra-skull, and intraspinal lipomas. We hereby present a case of CMN syndrome in an 18-year-old girl with leptomeningeal melanoma, evaluated with MRI, adequately staged, and screened with FDG PET.
机构:
Univ Texas Austin, Dell Med Sch, Dept Pediat, Div Pediat Dermatol, 1301 Barbara Jordan Blvd,Suite 200A, Austin, TX 78723 USAUniv Texas Austin, Dell Med Sch, Dept Pediat, Div Pediat Dermatol, 1301 Barbara Jordan Blvd,Suite 200A, Austin, TX 78723 USA