B-cell lymphoma in a patient with WHIM syndrome

被引:41
|
作者
Chae, KM [1 ]
Ertle, JO [1 ]
Tharp, MD [1 ]
机构
[1] Rush Presbyterian St Lukes Med Ctr, Dept Dermatol, Chicago, IL 60612 USA
关键词
D O I
10.1067/mjd.2001.111337
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
WHIM syndrome is a rare congenital familial syndrome consisting of warts, hypogammaglobulinemia, infections, and myelokathexis. We describe a 30-year-old man with WHIM syndrome, in whom red dermal facial nodules developed. The diagnosis of B-cell lymphoma was established with biopsy and immunohistochemical studies. To our knowledge, this is the first reported case of WHIM syndrome complicated by a B-cell lymphoma.
引用
收藏
页码:124 / 128
页数:5
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