Collagen type VI deficiency disrupts basal lamina-extracellular matrix binding in Ullrich congenital muscular dysytrophy and COL6A1 null mutant skeletal muscle

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作者
Sabatelli, P
Bonaldo, P
Columbaro, M
Mura, I
Mattioli, E
Bertini, E
Pepe, G
Guicheney, P
Merlini, L
Squarzoni, S
机构
[1] CNR, ITOI, IOR, I-40126 Bologna, Italy
[2] Univ Padua, Dept Histol, Padua, Italy
[3] IOR, Neuromuscular Unit, Bologna, Italy
[4] Bambino Gesu Hosp IRCCS, Rome, Italy
[5] Univ Florence, Florence, Italy
[6] INSERM, U582, Paris, France
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R74 [神经病学与精神病学];
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页码:647 / 647
页数:1
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