Focal segmental glomerulosclerosis in association with Gitelman syndrome

被引:6
|
作者
Ceri, Mevlut [1 ]
Unverdi, Selman [1 ]
Altay, Mustafa [2 ]
Unverdi, Hatice [3 ]
Kurultak, Ilhan [4 ]
Yilmaz, Rahmi [1 ]
Ensari, Arzu [3 ]
Duranay, Murat [1 ]
机构
[1] Ankara Educ & Res Hosp, Dept Nephrol, Ankara, Turkey
[2] Ankara Educ & Res Hosp, Dept Internal Med, Ankara, Turkey
[3] Ankara Univ, Dept Pathol, Fac Med, TR-06100 Ankara, Turkey
[4] Ankara Univ, Dept Nephrol, Fac Med, TR-06100 Ankara, Turkey
关键词
Gitelman syndrome; Proteinuria; Focal segmental glomerulosclerosis; HYPOKALEMIC ALKALOSIS; EXPRESSION; KIDNEY;
D O I
10.1007/s11255-010-9802-z
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Gitelman syndrome (GS) is an autosomal recessive disorder characterized by hypokalemia, metabolic alkalosis, hypomagnesemia and hypocalciuria. Glomerulonephritis associated with GS is rarely documented in the literature. We present an adult patient with GS whose renal biopsy revealed focal segmental glomerulosclerosis.
引用
收藏
页码:905 / 907
页数:3
相关论文
共 50 条
  • [1] Focal segmental glomerulosclerosis in association with Gitelman syndrome
    Mevlut Ceri
    Selman Unverdi
    Mustafa Altay
    Hatice Unverdi
    Ilhan Kurultak
    Rahmi Yılmaz
    Arzu Ensari
    Murat Duranay
    [J]. International Urology and Nephrology, 2011, 43 : 905 - 907
  • [2] Association of Gitelman's syndrome and focal glomerulosclerosis
    Bulucu, F
    Vural, A
    Yenicesu, M
    Çaglar, K
    [J]. NEPHRON, 1998, 79 (02): : 244 - 244
  • [3] Hypokalaemic metabolic alkalosis resembing Gitelman syndrome with focal segmental glomerulosclerosis
    Brebner, Alex
    Hayat, Ashik
    [J]. INTERNAL MEDICINE JOURNAL, 2017, 47 (10) : 1211 - 1213
  • [4] Marfan Syndrome and Focal Segmental Glomerulosclerosis: a Novel Association
    Gupta, Ankur
    Gaikwad, Jyoti
    Khaira, Ambar
    Rana, Devender S.
    [J]. SAUDI JOURNAL OF KIDNEY DISEASES AND TRANSPLANTATION, 2010, 21 (04) : 754 - 755
  • [5] Guillain-Barre syndrome in association with focal segmental glomerulosclerosis
    Heckmann, JG
    Böhmer, K
    Druschky, A
    Winterholler, M
    Neundörfer, B
    [J]. EUROPEAN NEUROLOGY, 1998, 40 (02) : 114 - 115
  • [6] FOCAL SEGMENTAL GLOMERULOSCLEROSIS (FSGS) WITH GITELMAN'S SYNDROME (GS): CASE REPORT, TREATMENT AND OUTCOMES
    Olaniran, Kabir
    Kim, Susan
    Venugopal, Usha
    Kumar, Neeraj
    [J]. AMERICAN JOURNAL OF KIDNEY DISEASES, 2014, 63 (05) : A84 - A84
  • [7] Kartagener Syndrome With Focal Segmental Glomerulosclerosis
    Momeni, Ali
    Doroushi, Behzad
    Taheri, Nadia
    [J]. IRANIAN JOURNAL OF KIDNEY DISEASES, 2013, 7 (06) : 499 - 501
  • [8] DUANES SYNDROME AND FOCAL SEGMENTAL GLOMERULOSCLEROSIS
    SATO, H
    SAITO, T
    OOTAKA, T
    YAMAKAGE, K
    FURUYAMA, T
    YOSHINAGA, K
    [J]. NEPHRON, 1989, 51 (02): : 274 - 275
  • [9] Focal segmental glomerulosclerosis and Turner syndrome
    Wattad, A
    Jain, J
    Kerrigan, J
    Youngberg, G
    [J]. NEPHRON, 1998, 80 (01): : 106 - 106
  • [10] PHEOCHROMOCYTOMA AND THE ECTOPIC CORTICOTROPIN SYNDROME IN ASSOCIATION WITH FOCAL SEGMENTAL GLOMERULOSCLEROSIS AND THE NEPHROTIC SYNDROME
    CHAN, R
    MICHELIS, MF
    [J]. AMERICAN JOURNAL OF KIDNEY DISEASES, 1992, 19 (03) : 289 - 291