Persistent pulmonary hypertension of newborn due to congenital capillary alveolar dysplasia

被引：21
|
作者：
Singh, SA
Ibrahim, T
Clark, DJ
Taylor, RS
George, DH
机构：
[1] Univ Calgary, Foothills Med Ctr, Dept Pathol, Calgary, AB T2N 2T9, Canada
[2] Univ Calgary, Foothills Med Ctr, Dept Neonatol, Calgary, AB T2N 2T9, Canada
来源：
PEDIATRIC PULMONOLOGY | 2005年 / 40卷 / 04期
关键词：
alveolar capillary dysplasia; persistent pulmonary hypertension; neonate;
D O I：
10.1002/ppul.20244
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
Congenital alveolar capillary dysplasia is a rare and fatal cause of pulmonary hypertension in neonates. We report on a term baby with severe pulmonary hypertension unresponsive to high-frequency ventilation and nitric oxide. A diagnosis of alveolar capillary dysplasia was established on autopsy We review the literature regarding pathophysiology, clinical presentations, associated malformations, and treatment trials.
引用
收藏
页码：349 / 353
页数：5
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