Use of recombinant factor viia for bleeding in children with Glanzmann thrombasthenia
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作者:
Çaglar, K
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Hacettepe Univ, Fac Med, Dept Pediat, Pediat Hematol Unit, TR-06100 Ankara, TurkeyHacettepe Univ, Fac Med, Dept Pediat, Pediat Hematol Unit, TR-06100 Ankara, Turkey
Çaglar, K
[1
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Çetinkaya, A
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Hacettepe Univ, Fac Med, Dept Pediat, Pediat Hematol Unit, TR-06100 Ankara, TurkeyHacettepe Univ, Fac Med, Dept Pediat, Pediat Hematol Unit, TR-06100 Ankara, Turkey
Çetinkaya, A
[1
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Aytaç, S
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Hacettepe Univ, Fac Med, Dept Pediat, Pediat Hematol Unit, TR-06100 Ankara, TurkeyHacettepe Univ, Fac Med, Dept Pediat, Pediat Hematol Unit, TR-06100 Ankara, Turkey
Aytaç, S
[1
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Gümrük, F
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Hacettepe Univ, Fac Med, Dept Pediat, Pediat Hematol Unit, TR-06100 Ankara, TurkeyHacettepe Univ, Fac Med, Dept Pediat, Pediat Hematol Unit, TR-06100 Ankara, Turkey
Gümrük, F
[1
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Gürgey, A
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Hacettepe Univ, Fac Med, Dept Pediat, Pediat Hematol Unit, TR-06100 Ankara, TurkeyHacettepe Univ, Fac Med, Dept Pediat, Pediat Hematol Unit, TR-06100 Ankara, Turkey
Gürgey, A
[1
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机构:
[1] Hacettepe Univ, Fac Med, Dept Pediat, Pediat Hematol Unit, TR-06100 Ankara, Turkey
Glanzmann thrombasthenia is a very rare inherited platelet function disorder in which bleeding may be extremely difficult to stop. Recombinant factor VIIa is one of the alternative treatments for bleeding. The authors report here their experience with the use of factor VIIa, which may be useful for arresting bleeding in Glazmann thrombasthenia.