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Copenhagen Univ Hosp, Danish PCD & chILD Ctr, Dept Paediat & Adolescent Med, Paediat Pulm Serv,Rigshosp,CF Ctr Copenhagen, Blegdamsvej 9, DK-2100 Copenhagen, Denmark Copenhagen Univ Hosp, Danish PCD & chILD Ctr, Dept Paediat & Adolescent Med, Paediat Pulm Serv,Rigshosp,CF Ctr Copenhagen, Blegdamsvej 9, DK-2100 Copenhagen, Denmark