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Claude Bernard Univ Lyon 1, Hosp Civils Lyon, Natl Reference Ctr Rare Pulm Dis, Louis Pradel Hosp,Dept Resp Med,UMR 754, Lyon, France Claude Bernard Univ Lyon 1, Hosp Civils Lyon, Natl Reference Ctr Rare Pulm Dis, Louis Pradel Hosp,Dept Resp Med,UMR 754, Lyon, France