A malignant peripheral nerve sheath tumor of the mediastinum in a patient with neurofibromatosis type 1: Report of a case

被引：4
|
作者：
Kawachi, Riken [1 ]
Takei, Hidefumi [1 ]
Furuyashiki, Goh [1 ]
Koshi-Ishi, Yoshihiko [1 ]
Goya, Tomoyuki [1 ]
机构：
[1] Kyorin Univ, Sch Med, Gen Thorac Surg Div, Dept Surg, Tokyo 1818611, Japan
来源：
SURGERY TODAY | 2008年 / 38卷 / 10期
关键词：
malignant peripheral nerve sheath tumor; neurofibromatosis type 1; von Recklinghausen's disease; mediastinal tumor;
D O I：
10.1007/s00595-008-3764-0
中图分类号：
R61 [外科手术学];
学科分类号：
摘要：
Malignant peripheral nerve sheath tumor (MPNST) is rare, but its association with neurofibromatosis type 1 (NF1) is well known. A 56-year-old man with NF1 was referred to our hospital for investigation of dyspnea. Computed tomography showed a huge mass occupying the right thorax and invading the inferior vena cava. A salvage resection was performed to alleviate the developing hypoxemia. Histological examination confirmed an MPNST. The tumor regrew rapidly and the patient died 6 weeks after the resection. This case report reinforces the importance of monitoring patients with NF1 carefully because of their increased risk of the development of malignant neoplasms.
引用
收藏
页码：945 / 947
页数：3
相关论文
共 50 条
  • [1] A malignant peripheral nerve sheath tumor of the mediastinum in a patient with neurofibromatosis type 1: Report of a case
    Riken Kawachi
    Hidefumi Takei
    Goh Furuyashiki
    Yoshihiko Koshi-Ishi
    Tomoyuki Goya
    Surgery Today, 2008, 38 : 945 - 947
  • [2] Pseudoprogression of Malignant Peripheral Nerve Sheath Tumor in Patient with Neurofibromatosis Type 1, a Case Report
    Lessing, Andres J.
    Cote, Gregory M.
    DeLaney, Thomas F.
    Plotkin, Scott R.
    Raskin, Kevin A.
    Lessing, Juan N.
    CASE REPORTS IN ONCOLOGY, 2021, 14 (03): : 1342 - 1346
  • [3] Metastatic malignant peripheral nerve sheath tumor in neurofibromatosis Type 1: a geriatric patient report
    Firat, C.
    Aytekin, A. H.
    Erbatur, S.
    EUROPEAN REVIEW FOR MEDICAL AND PHARMACOLOGICAL SCIENCES, 2012, 16 (09) : 1301 - 1304
  • [4] Mediastinal Malignant Peripheral Nerve Sheath Tumor in a Neurofibromatosis Type 1 Patient
    Alexander Diaz-Perez, Julio
    Ferreira Bohorquez, Edgar Julian
    INTERNATIONAL JOURNAL OF MORPHOLOGY, 2011, 29 (01): : 133 - 139
  • [5] A Case Report of a Malignant Peripheral Nerve Sheath Tumor of the Oral Cavity in Neurofibromatosis Type 1
    Ozturk, Ozmen
    Tutkun, Alper
    CASE REPORTS IN OTOLARYNGOLOGY, 2012, 2012
  • [6] A case of malignant peripheral nerve sheath tumor in a young patient with neurofibromatosis 1
    Tofuku, Yukari
    Ota, Arihito
    Ito, Munenari
    Umezawa, Yoshinori
    Nakagawa, Hidemi
    JOURNAL OF DERMATOLOGY, 2012, 39 : 100 - 100
  • [7] Recurrent malignant peripheral nerve sheath tumour in a patient with neurofibromatosis Type 1: A case report
    Dimou, J.
    Jithoo, R.
    Pitcher, M.
    White, G.
    JOURNAL OF CLINICAL NEUROSCIENCE, 2009, 16 (09) : 1221 - 1223
  • [8] Malignant peripheral nerve sheath tumor in the anterior mediastinum: A case report
    Koezuka, Satoshi
    Hata, Yoshinobu
    Sato, Fumitomo
    Otsuka, Hajime
    Makino, Takashi
    Tochigi, Naobumi
    Iyoda, Akira
    MOLECULAR AND CLINICAL ONCOLOGY, 2014, 2 (06) : 987 - 990
  • [9] Malignant Peripheral Nerve Sheath Tumor in Neurofibromatosis Type 1
    Rossiter, John P.
    Fenton, Paul V.
    JAMA NEUROLOGY, 2014, 71 (02) : 241 - 241
  • [10] Small intestine gastrointestinal stromal tumor and malignant peripheral nerve sheath tumor in a patient with neurofibromatosis type 1: A case report
    Lin, Yu-Hung
    Wang, Chun-Hsiang
    Chiu, Yin-, I
    Lin, Ruey-Chang
    Mo, Lein-Ray
    ADVANCES IN DIGESTIVE MEDICINE, 2021, 8 (04) : 241 - 244
12345