MR cholangiography in the diagnosis of sclerosing cholangitis in Langerhans' cell histiocytosis

被引:14
|
作者
König, CW
Pfannenberg, C
Trübenbach, J
Remy, C
Böhmer, GM
Ruck, P
Claussen, CD
机构
[1] Univ Tubingen, Dept Diagnost Radiol, D-72076 Tubingen, Germany
[2] Univ Tubingen, Dept Gastroenterol, D-72076 Tubingen, Germany
[3] Univ Tubingen, Inst Pathol, D-72076 Tubingen, Germany
关键词
Langerhans' cell histiocytosis; sclerosing cholangitis; MR cholangiopancreatography;
D O I
10.1007/s003300100835
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Langerhans' cell histiocytosis (LCH) is a disorder of histiocytic proliferation that primarily affects infants. Imaging findings of a rare case of lung and liver involvement in an adult are presented. High-resolution computed tomography (HRCT) of the lungs showed confluent thin-walled cystic air spaces compatible with advanced LCH. Liver CT and MRI revealed unspecific signs of fatty infiltration. Irregular widening of peripheral bile ducts was displayed in breath-hold MR cholangiography. This pattern is considered characteristic for sclerosing cholangitis and should support the diagnosis of LCH in case of concomitant cystic pulmonary disease, even in adult patients.
引用
收藏
页码:2516 / 2520
页数:5
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