[1] Claude Bernard Univ Lyon 1, Natl Reference Ctr Rare Pulm Dis, Hosp Civils Lyon, Louis Pradel Hosp, Lyon, France
[2] Univ British Columbia, Dept Med, Vancouver, BC, Canada
[3] Univ British Columbia, Ctr Heart Lung Innovat, Vancouver, BC, Canada
[4] Univ Michigan, Ann Arbor, MI 48109 USA
[5] Univ Colorado Denver, Dept Med, Aurora, CO USA
[6] Royal Prince Alfred Hosp, Camperdown, NSW, Australia
[7] Univ Sydney, Sydney, NSW, Australia
[8] Boehringer Ingelheim Int GmbH, Ingelheim, Germany
[9] Royal Brompton Hosp, Natl Inst Hlth Res Resp Biomed Res Unit, London, England
[10] Harefield NHS Fdn Trust, London, England
[11] Imperial Coll, Natl Heart & Lung Inst, London, England