Double pathology in Rasmussen's encephalitis: Etiologic considerations

被引:31
|
作者
Yacubian, EMT
Rosemberg, S
Marie, SKN
Valerio, RMF
Jorge, CL
Cukiert, A
机构
[1] UNIV SAO PAULO,SCH MED,DEPT NEUROL,DIV NEUROPATHOL,BR-05508 SAO PAULO,BRAZIL
[2] UNIV SAO PAULO,SCH MED,DEPT NEUROSURG,DIV NEUROPATHOL,BR-05508 SAO PAULO,BRAZIL
[3] UNIV SAO PAULO,SCH MED,DEPT PATHOL,DIV NEUROPATHOL,BR-05508 SAO PAULO,BRAZIL
关键词
epilepsia partialis continua; Rasmussen's syndrome; double pathology;
D O I
10.1111/j.1528-1157.1996.tb00597.x
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
In a 7-year-old girl with epilepsia partialis continua (EPC) involving the left face, arm, and leg for 1 year, serial neuroimaging studies showed progressive, brain atrophy. Because medical treatment was ineffective, she underwent a large fronto-temporal surgical resection. Neuropathological examination showed loss of lamination and dysplastic neurons, gliosis, microglial nodules, and perivascular cuffing. Such ''double pathology'' (dysgenesia and a chronic inflammatory process) may have implications for the pathophysiology of Rasmussen's syndrome.
引用
收藏
页码:495 / 500
页数:6
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