Acrodermatitis enteropathica

被引:0
|
作者
Alvarez, Pilar
Pais, Maria E.
Hernandez, Marisa
Soliani, Andrea
Garcia Diaz, Rita
机构
来源
ARCHIVOS ARGENTINOS DE PEDIATRIA | 2007年 / 105卷 / 06期
关键词
acrodermatitis enteropathica; zinc;
D O I
暂无
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Acrodermatitis enteropathica is a rare autosomal recesive disorder, caused by impaired absorption of zinc dietary intake. It is characterized by a triad of alopecia, diarrhea and acral and periorificial dermatitis. We report an 11 month-old girl with tipical symptoms in whom, the diagnosis was confirmed by decreased plasma zinc level (37,7 mu g%). The patient was given zinc sulfate 5 mg/kg/day and showed marked improvement.
引用
收藏
页码:536 / 538
页数:3
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