Schnitzler syndrome: A review of literature, the authors' observation, and experience with the interleukin-1 inhibitor canakinumab

被引:2
|
作者
Salugina, S. O. [1 ]
Gorodetsky, V. R. [1 ]
Fedorov, E. S. [1 ]
Lopatina, N. E. [1 ]
Evsikova, M. D. [1 ]
机构
[1] VA Nasonova Res Inst Rheumatol, Moscow, Russia
关键词
autoinflammatory diseases; Schnitzler syndrome; therapy; IL-1; inhibitors; canakinumab; CHRONIC URTICARIA; FOLLOW-UP; ANAKINRA; MACROGLOBULINEMIA; GAMMOPATHY; DISEASE; SAFETY;
D O I
10.17116/terarkh20178911111-115
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
The paper reviews the publications dealing with Schnitzler syndrome, a rare autoinflammatory disease, and describes the authors' own clinical observation. It describes the first Russian experience in successfully using the interleukin-1 inhibitor canakinumab to treat this disease.
引用
收藏
页码:111 / 115
页数:7
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