Inflammatory pseudotumor-like follicular/fibroblastic dendritic cell sarcoma: focus on immunohistochemical profile and association with Epstein-Barr virus

被引:12
|
作者
Pagliuca, Francesca [1 ]
Ronchi, Andrea [1 ]
Auricchio, Annamaria [2 ]
Lieto, Eva [2 ]
Franco, Renato [1 ]
机构
[1] Univ Campania Luigi Vanvitelli, Dept Mental & Phys Hlth & Prevent Med, Pathol Unit, Via Luciano Armanni 5, I-80100 Naples, Italy
[2] Univ Campania Luigi Vanvitelli, Dept Translat Med Sci, Div Gastrointestinal Tract Surg Oncol, I-80138 Naples, Italy
关键词
Inflammatory pseudotumour-like follicular; fibroblastic dendritic cell sarcoma; Epstein-Barr virus; Immunohistochemistry; SPLEEN; TUMOR;
D O I
10.1186/s13027-022-00474-8
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Inflammatory pseudotumour-like follicular/fibroblastic dendritic cell sarcoma (IPT-like FDCS) is a rare EBV-associated variant of follicular dendritic cell sarcoma, usually arising in the liver or spleen and characterized by a favourable prognosis. The neoplastic cells show variable follicular dendritic cell or fibroblastic reticular cell differentiation and their immunoprofile is still poorly characterized. We describe a case of splenic IPT-like FDCS with unexpected CD31 expression and provide a concise review of English literature on the topic.
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页数:5
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