Treatment of the Patient With Crouzon Syndrome With Orthognathic Surgery

Crouzon syndrome is a genetic disease that is transferred by autosomal dominant inheritance. Patients with this syndrome have craniosynostosis, hypertelorism, orbital proptosis, mid-face hypoplasia, mandibular prognathism, and concave facial profile. A number of surgical treatments are used to improve facial contours, and to correct dental and maxillary relationships. Orthognathic surgery is routinely used in the treatment of these patients. We present a female patient with Crouzon syndrome treated with Le Fort I and bilateral sagittal split osteotomy. Previously, surgically assisted rapid maxillary expansion (SARME) surgery was performed to the patient by separating the pterygomaxillary junction under general anesthesia. Down fracture was performed during the Le Fort I osteotomy without the need to separate the pterygomaxillary junction again. The facial appearance was improved with bilateral sagittal split osteotomy, and skeletal malocclusion between the jaws was treated.