Population-based review of tetralogy of Fallot with absent pulmonary valve: is prenatal diagnosis really associated with a poor prognosis?

被引:6
|
作者
Mivelaz, Y. [2 ]
Lim, K. I. [2 ,4 ]
Templeton, C. [2 ]
Campbell, A. I. [2 ,3 ]
Potts, J. E. [2 ]
Sandor, G. G. S. [1 ,2 ]
机构
[1] British Columbia Childrens Hosp, Childrens Heart Ctr, Dept Pediat, Div Cardiol, Vancouver, BC V6H 3V4, Canada
[2] Univ British Columbia, Vancouver, BC V5Z 1M9, Canada
[3] British Columbia Childrens Hosp, Dept Surg, Div Cardiac Surg, Vancouver, BC V6H 3V4, Canada
[4] British Columbia Womens Hosp, Dept Obstet & Gynaecol, Div Maternal Fetal Med, Vancouver, BC, Canada
关键词
absent pulmonary valve syndrome; congenital heart disease; fetal; outcome; prenatal diagnosis; tetralogy of Fallot; OUTCOMES; REPAIR;
D O I
10.1002/uog.11126
中图分类号
O42 [声学];
学科分类号
070206 ; 082403 ;
摘要
Objectives Tetralogy of Fallot with absent pulmonary valve syndrome (TETAPV) is reported in obstetric literature to have an extremely poor prognosis. We sought to determine the clinical outcome associated with TETAPV and whether prenatal diagnosis confers a poor prognosis. Methods All cases of TETAPV diagnosed in British Columbia between 1980 and 2009 were reviewed and grouped according to time of diagnosis, either prenatal or postnatal. The groups were compared with respect to mortality, respiratory problems, number of interventions and functional capacity at last follow-up. Results Eight and 11 patients were included in the prenatally and postnatally diagnosed groups, with overall long-term survival of 71% and 82%, respectively. There was no significant difference in mortality, frequency of preoperative intubation, number of interventions or functional capacity between groups. Conclusion From a population-based retrospective analysis of TETAPV cases identified over three decades it is concluded that the prognosis for TETAPV is better than that previously reported in the obstetric literature. This information should be used to guide prenatal counseling. Copyright. (C) 2012 ISUOG. Published by John Wiley & Sons, Ltd.
引用
收藏
页码:536 / 541
页数:6
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