Atypical pulmonary artery sling with diffuse-type pulmonary arteriovenous fistula

被引:0
|
作者
Huh, J
Choi, JY
Kim, YW
Noh, CI
Yun, YS
Son, CS
Tockgo, YC
机构
[1] Seoul Natl Univ, Coll Med, Cardiol Sect, Dept Pediat, Seoul, South Korea
[2] Korea Univ, Coll Med, Dept Pediat, Seoul 136701, South Korea
关键词
pulmonary artery sling; arteriovenous fistula;
D O I
10.3346/jkms.1999.14.1.80
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
The case of a cyanotic infant with a rare combination of atypical pulmonary artery sling, imperforate anus, absence of the left kidney, interruption of the inferior vena cava, left side hemihypertrophy and diffuse-type pulmonary arteriovenous fistula is described. The clinical features were confusing, because of compounding abnormalities involving the respiratory tract and pulmonary circulation. The diagnostic approach to the etiology of cyanosis is discussed and the embryonic origin of pulmonary artery sling is reviewed.
引用
收藏
页码:80 / 84
页数:5
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