Rare cause of a resistant hypertension in a middle-aged man: A case report

被引:0
|
作者
Marecek, Renata [1 ]
De Keyzer, Eva [2 ]
Taujan, Georgiana [3 ]
Baleanu, Felicia [3 ]
Rosu, Mihaela [3 ]
Papadopoulou, Ioanna [3 ]
Kosmopoulou, Olga [3 ]
Laura, Iconaru [3 ]
机构
[1] Univ Libre Bruxelles, Ctr Hospitalier Univ Brugmann, Dept Internal Med, Brussels, Belgium
[2] Univ Libre Bruxelles, Ctr Hospitalier Univ Brugmann, Dept Cardiol, Brussels, Belgium
[3] Univ Libre Bruxelles, Ctr Hospitalier Univ Brugmann, Dept Endocrinol, Brussels, Belgium
来源
CLINICAL CASE REPORTS | 2022年 / 10卷 / 12期
关键词
11-b-hydroxylase deficiency; congenital adrenal hyperplasia; secondary hypertension; testicular adrenal rest tumors; CONGENITAL ADRENAL-HYPERPLASIA; 11-BETA-HYDROXYLASE DEFICIENCY; MUTATIONS; VARIABILITY; REST;
D O I
10.1002/ccr3.6606
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Congenital adrenal hyperplasia associated to 11-beta-hydroxylase deficiency is a rare cause of secondary hypertension, usually discovered during childhood; however, a late diagnosis in adults has also been reported. Despite low cortisol levels, accumulated adrenal steroid precursors can activate the glucocorticoid receptor and thus protect the patient against adrenal crisis.
引用
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页数:5
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