Alterations of arginine in Lysinuric Protein Intolerance (LPI) macrophages

被引:0
|
作者
Barilli, Amelia [1 ]
Rotoli, Bianca Maria [1 ]
Visigalli, Rossana [1 ]
Dall'Asta, Valeria [1 ]
机构
[1] Univ Parma, SBiBiT, I-43100 Parma, Italy
来源
FASEB JOURNAL | 2013年 / 27卷
关键词
D O I
暂无
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
lb475
引用
下载
收藏
页数:1
相关论文
共 50 条
  • [1] CUGC for lysinuric protein intolerance (LPI)
    Diego Martinelli
    Manuel Schiff
    Michela Semeraro
    Emanuele Agolini
    Antonio Novelli
    Carlo Dionisi-Vici
    European Journal of Human Genetics, 2020, 28 : 1129 - 1134
  • [2] CUGC for lysinuric protein intolerance (LPI)
    Martinelli, Diego
    Schiff, Manuel
    Semeraro, Michela
    Agolini, Emanuele
    Novelli, Antonio
    Dionisi-Vici, Carlo
    EUROPEAN JOURNAL OF HUMAN GENETICS, 2020, 28 (08) : 1129 - 1134
  • [3] Macrophages from patients affected by Lysinuric Protein Intolerance (LPI) exhibit an impaired phagocytosis
    Rotoli, Bianca Maria
    Barilli, Amelia
    Visigalli, Rossana
    Dall'Asta, Valeria
    FASEB JOURNAL, 2012, 26
  • [4] FIRST POLISH CASES WITH LYSINURIC PROTEIN INTOLERANCE (LPI)
    Rokicki, D.
    Pronicka, E.
    JOURNAL OF INHERITED METABOLIC DISEASE, 2005, 28 : 254 - 254
  • [5] LYSINURIC PROTEIN INTOLERANCE (LPI) - TREATMENT WITH CITRULLINE AND LYSINE
    RAJANTIE, J
    SIMELL, O
    PERHEENTUPA, J
    PEDIATRIC RESEARCH, 1979, 13 (01) : 78 - 78
  • [6] LYSINURIC PROTEIN INTOLERANCE (LPI): EXPERIENCE OF A GREEK CENTER
    Augoustides-Savvopoulou, P.
    Ioannou, C.
    JOURNAL OF INHERITED METABOLIC DISEASE, 2011, 34 : S85 - S85
  • [7] ARGININE SUPPLEMENTATION IN LYSINURIC PROTEIN INTOLERANCE
    ANDRIA, G
    SEBASTIO, G
    SARTORIO, R
    SANNOLO, N
    JOURNAL OF INHERITED METABOLIC DISEASE, 1982, 5 : 61 - 62
  • [8] OROTIC ACIDURIA, AN INDICATOR OF ADEQUACY OF TREATMENT IN LYSINURIC PROTEIN INTOLERANCE (LPI)
    RAJANTIE, J
    SIMELL, O
    PERHEENTUPA, J
    PEDIATRIC RESEARCH, 1980, 14 (02) : 177 - 177
  • [9] LYSINURIC PROTEIN INTOLERANCE (LPI) - ATYPICAL SYNDROMES, DIAGNOSTIC PROBLEMS AND COURSE
    SCHUBERT, E
    BACHMANN, C
    MONATSSCHRIFT KINDERHEILKUNDE, 1985, 133 (08) : 606 - 606
  • [10] TRANSPORT OF HOMOARGININE INTO LIVER SLICES OF PATIENTS WITH LYSINURIC PROTEIN INTOLERANCE (LPI)
    SIMELL, O
    PERHEENTUPA, J
    PEDIATRIC RESEARCH, 1974, 8 (11) : 904 - 904