Is ALS caused by an altered oxidative activity of mutant superoxide dismutase?

被引:28
|
作者
Bush, AI
机构
[1] Massachusetts Gen Hosp, Lab Oxidat Biol, Genet & Aging Res Unit, Charlestown, MA 02129 USA
[2] Univ Melbourne, Dept Pathol, Parkville, Vic 3052, Australia
[3] Univ Melbourne, Mental Hlth Res Inst, Oxidat Disorders Lab, Parkville, Vic 3052, Australia
关键词
D O I
10.1038/nn1002-919a
中图分类号
Q189 [神经科学];
学科分类号
071006 ;
摘要
引用
收藏
页码:919 / 919
页数:1
相关论文
共 50 条
  • [1] Is ALS caused by an altered oxidative activity of mutant superoxide dismutase?
    Ashley I. Bush
    Nature Neuroscience, 2002, 5 : 919 - 919
  • [2] Reply to 'Is ALS caused by an altered oxidative activity of mutant superoxide dismutase?'
    Philip C. Wong
    Nature Neuroscience, 2002, 5 : 919 - 920
  • [3] SUPEROXIDE-DISMUTASE ACTIVITY AND MARKERS OF OXIDATIVE DAMAGE IN SPORADIC AND FAMILIAL ALS
    BOWLING, AC
    BROWN, RH
    BEAL, MF
    NEUROLOGY, 1994, 44 (04) : A256 - A256
  • [4] THE ROLE OF MICROGLIA IN ALS CAUSED BY SUPEROXIDE DISMUTASE MUTATIONS
    Julien, J. P.
    Gowing, G.
    GLIA, 2009, 57 (13) : S17 - S18
  • [5] Aggregation of ALS mutant superoxide dismutase expressed in Escherichia coli
    Leinweber, B
    Barofsky, E
    Barofsky, DF
    Ermilov, V
    Nylin, K
    Beckman, JS
    FREE RADICAL BIOLOGY AND MEDICINE, 2004, 36 (07) : 911 - 918
  • [6] Variants of superoxide dismutase with altered nitration activity
    Keng, T
    Jain, S
    Privalle, CT
    BIOLOGY OF NITRIC OXIDE, PT 5, 1996, 10 : 113 - 113
  • [7] SUPEROXIDE-DISMUTASE AND ALS
    ORRELL, RW
    DEBELLEROCHE, JS
    LANCET, 1994, 344 (8938): : 1651 - 1652
  • [8] Misfolded superoxide dismutase and ALS
    Hart, PJ
    Elam, JS
    Taylor, AB
    Strange, R
    Hasnain, SS
    Doucette, PA
    Valentine, JS
    Hayward, LJ
    JOURNAL OF INORGANIC BIOCHEMISTRY, 2003, 96 (01) : 44 - 44
  • [9] THE EFFECTS OF GENETICALLY ALTERED SUPEROXIDE-DISMUTASE ACTIVITY
    EPSTEIN, CJ
    HUANG, TT
    CHAN, PH
    CADET, JL
    CARLSON, EJ
    JOURNAL OF CELLULAR BIOCHEMISTRY, 1994, : 185 - 185
  • [10] Aggregation of mutant Cu/Zn superoxide dismutase proteins in a culture model of ALS
    Durham, HD
    Roy, J
    Dong, L
    Figlewicz, DA
    JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1997, 56 (05): : 523 - 530