Primary Ciliary Dyskinesia and Bronchiectasis: New Data and Future Challenges

被引:3
|
作者
Pioch, Charlotte O. [1 ]
Connell, David W. [2 ]
Shoemark, Amelia [2 ,3 ]
机构
[1] Charite Univ Med Berlin, Dept Pediat Resp Med Immunol & Crit Care Med, Berlin, Germany
[2] Univ Dundee, Scottish Ctr Resp Res, Div Mol & Clin Med, Dundee, Angus, Scotland
[3] Royal Brompton Hosp, PCD Diagnost Serv, London, England
来源
ARCHIVOS DE BRONCONEUMOLOGIA | 2023年 / 59卷 / 03期
关键词
D O I
10.1016/j.arbres.2022.12.001
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
引用
收藏
页码:134 / 136
页数:3
相关论文
共 50 条
  • [1] Primary Ciliary Dyskinesia in Adult Bronchiectasis Data from the German Bronchiectasis Registry PROGNOSIS
    Ewen, Raphael
    Pink, Isabell
    Sutharsan, Sivagurunathan
    Aries, Sven P.
    Gruenewaldt, Achim
    Shoemark, Amelia
    Sommerwerck, Urte
    Staar, Ben O.
    Wege, Sabine
    Mertsch, Pontus
    Rademacher, Jessica
    Ringshausen, Felix C.
    CHEST, 2024, 166 (05) : 938 - 950
  • [2] Primary ciliary dyskinesia in adults with bronchiectasis: Data from the Embarc registry
    Shoemark, Amelia
    Polverino, Eva
    Blasi, Francesco
    Ringshausen, Felix C.
    De Soyza, Anthony
    Vendrell, Montserrat
    Goeminne, Pieter C.
    Boersma, Wim
    Haworth, Charles S.
    Murris, Marlene
    Dimakou, Katerina
    Hill, Adam T.
    Loebinger, Micheal R.
    Menendez, Rosario
    Torres, Antoni
    Welte, Tobias
    Wilson, Robert
    Elborn, Stuart
    Alberti, Stefano
    Chalmers, James D.
    EUROPEAN RESPIRATORY JOURNAL, 2018, 52
  • [3] Genetic causes of bronchiectasis: Primary ciliary dyskinesia
    Morillas, Hilda N.
    Zariwala, Maimoona
    Knowles, Michael R.
    RESPIRATION, 2007, 74 (03) : 252 - 263
  • [4] Morphological Analysis of Bronchiectasis in Primary Ciliary Dyskinesia
    Saito, M.
    Asakura, T.
    Gilmore, R. C.
    Chua, M.
    Randell, S. H.
    O'Neal, W. K.
    Boucher, R. C.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2024, 209
  • [5] CILIARY DEFECTS IN HEALTHY-SUBJECTS, BRONCHIECTASIS, AND PRIMARY CILIARY DYSKINESIA
    DEIONGH, RU
    RUTLAND, J
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 1995, 151 (05) : 1559 - 1567
  • [6] Assessment of Bronchiectasis by Impulse Oscillometry in Primary Ciliary Dyskinesia
    De Porras, P. M. Quiles Ruiz
    De Jesus-Rojas, W.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2022, 205
  • [7] Primary Ciliary Dyskinesia in a Portuguese Bronchiectasis Outpatient Clinic
    Tinoco, Eduarda Milheiro
    Gigante, Ana Rita
    Ferreira, Edite
    Sanches, Ines
    Pereira, Rute
    Sa, Rosalia
    Monteiro, Regina
    Sousa, Mario
    Pascoal, Ivone
    GENES, 2023, 14 (03)
  • [8] Is resection of bronchiectasis beneficial in patients with primary ciliary dyskinesia?
    Smit, HJM
    Schreurs, AJM
    VandenBosch, JMM
    Westermann, CJJ
    CHEST, 1996, 109 (06) : 1541 - 1544
  • [9] Lung Clearance Index in Primary Ciliary Dyskinesia and Bronchiectasis
    Irving, Samantha J.
    Davies, Jane C.
    Alton, Eric W. F.
    Bush, Andrew
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2014, 189 (09) : 1147 - 1148
  • [10] Primary ciliary dyskinesia: common cause of bronchiectasis in adults
    Simon, Annika
    PNEUMOLOGIE, 2025, 79 (02):