Microscopic polyangiitis initially presenting with idiopathic pulmonary fibrosis: a case report

被引:0
|
作者
Shao, Chi [1 ]
Chen, Ruxuan [1 ]
Huang, Hui [1 ]
Zhao, Yang [1 ]
Chen, Keqi [1 ]
Xu, Kai [2 ]
机构
[1] Chinese Acad Med Sci & Peking Union Med Coll, Peking Union Med Coll Hosp, Dept Pulm & Crit Care Med, Beijing, Peoples R China
[2] Chinese Acad Med Sci & Peking Union Med Coll, Peking Union Med Coll Hosp, Dept Radiol, Beijing, Peoples R China
关键词
usual interstitial pneumonia pattern; ANCA antibody; microscopic polyangiitis; antifibrotic therapy; idiopathic pulmonary fibrosis; CLASSIFICATION;
D O I
10.3389/fmed.2023.1157922
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Usual interstitial pneumonia is the most common type of microscopic polyangiitis (MPA)-associated interstitial lung disease, and patients may initially present with isolated pulmonary fibrosis, which often leads to a misdiagnosis of idiopathic pulmonary fibrosis (IPF). Here, we describe a patient who developed fever of unknown origin, microscopic hematuria and renal insufficiency, who then tested positive for antineutrophil cytoplasmic antibody (ANCA) and was diagnosed with MPA after receiving antifibrotic medication for IPF (original diagnosis) for almost 10 years. The patient's symptoms were ameliorated after administration of additional glucocorticoids and immunosuppressants.
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页数:5
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