Extrauterine Endometrial Stromal Sarcoma: A Case Report

Extrauterine endometrial stromal sarcomas are rare malignancies, with 181 cases reported so far. The basic predisposing factor is endometriosis, and ovary is the most common extrauterine site. Low-grade varieties are the most common subtypes encountered. Our patient is a young lady with low-grade extrauterine endometrial stromal sarcoma inoperable disease at presentation involving bilateral ovaries, omentum, peritoneum and hemorrhagic third space collections. The uterus was radiologically normal. She initially received palliative endocrine therapy and later underwent complete cytoreductive surgery. Currently, she is on an aromatase inhibitor.