Polycythemia as an Uncommon Finding in 2 Children, One With Systemic Capillary Leak Syndrome and the Other With Protein-losing Enteropathy Caused by CD55 Deficiency

被引：2
|
作者：
Kaya, Zuhre [1 ,3 ]
Derinoz, Oksan [2 ]
机构：
[1] Gazi Univ, Fac Med, Dept Pediat Hematol, Ankara, Turkiye
[2] Dept Pediat Emergency, Ankara, Turkiye
[3] Gazi Univ, Tip Fakultesi, Cocuk Sagligi & Hastaliklari Anabilim Dali, Cocuk Hematol Bilimdali, TR-06500 Ankara, Turkiye
来源：
JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY | 2023年 / 45卷 / 08期
关键词：
capillary leak syndrome; protein-losing enteropathy; polycythemia;
D O I：
10.1097/MPH.0000000000002729
中图分类号：
R73 [肿瘤学];
学科分类号：
100214 ;
摘要：
We report 2 children with distinct causes of polycythemia, 1 from systemic capillary leak syndrome (SCLS) and the other from protein-losing enteropathy (PLE) caused by CD55 deficiency. There is only a single case series about polycythemia in children with SCLS, but none on polycythemia in children with PLE. We present a 10-year-old girl with hypoalbuminemia, polycythemia, and edema who died as a result of an SCLS attack and a 1-year-old girl with PLE who was successfully treated with eculizumab. Our experience suggests that hematologists should be alert for SCLS and PLE in children with relative polycythemia.
引用
收藏
页码：E996 / E1000
页数：5
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