Oromandibular Limb Hypogenesis Syndrome Type IVB with Hypoglossia and Intraoral Band: A Case Report of a Rare Entity

The group of anomalies that affect the tongue, maxilla, and mandible-with or without limb anomalies-comes under the umbrella of the oromandibular limb hypogenesis syndrome. It is sporadically reported and has a very low incidence. There is no sex predilection for this congenital disease. We report a rare subtype of oromandibular limb hypogenesis syndrome in a young female who presented with impaired speech and deformity in the lower jaw.