Neuromyelitis Optica Spectrum Disorder: An Early Diagnosis to Prevent Blindness and Paraplegia

被引:0
|
作者
George, Minny [1 ]
Gantioque, Raymund [1 ]
机构
[1] Calif State Univ, Sch Nursing, 5151 State Univ Dr, Los Angeles, CA 90032 USA
来源
关键词
Devic's disease; monoclonal antibodies; neuromyelitis optica; neuromyelitis optica (NMO) antibody AQP4-IgG; neuromyelitis optica spectrum disorder; optic neuritis; transverse myelitis; MULTICENTER; EFFICACY; SAFETY; TRIAL;
D O I
10.1016/j.nurpra.2023.104654
中图分类号
R47 [护理学];
学科分类号
1011 ;
摘要
Neuromyelitis optica spectrum disorder (NMOSD), also referred to as Devic's disease, is a rare autoimmune disease of the central nervous system that primarily affects both the optic nerve (optic neuritis) and the spinal cord (myelitis). Patients presenting solely with optic neuritis or transverse myelitis can make diagnosis difficult. If left untreated, it may result in blindness and paralysis. Early and accurate diagnosis is crucial for treating and preventing further NMOSD attacks. This article describes the case of a previously healthy patient who presented with NMOSD. In addition, the clinical presentation, diagnostics, and treatment methods are discussed.& COPY; 2023 The Author(s). Published by Elsevier Inc. This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
引用
收藏
页数:4
相关论文
共 50 条
  • [1] Patient with paresthesia and paraplegia related to neuromyelitis optica spectrum disorder
    Rabadi, Meheroz H.
    AMERICAN JOURNAL OF THE MEDICAL SCIENCES, 2023, 366 (04): : E72 - E73
  • [2] Cortical Blindness: An Unusual Manifestation of Neuromyelitis Optica Spectrum Disorder
    Nagireddy, Ram Bhupal Reddy
    Kumar, Anand
    Kumar, Varun
    Pathak, Abhishek
    Joshi, Deepika
    ANNALS OF INDIAN ACADEMY OF NEUROLOGY, 2022, 25 (06) : 1246 - +
  • [3] Neuromyelitis Optica Spectrum Disorder
    Wingerchuk, Dean M.
    Lucchinetti, Claudia F.
    NEW ENGLAND JOURNAL OF MEDICINE, 2022, 387 (07): : 631 - 639
  • [4] NEUROMYELITIS OPTICA SPECTRUM DISORDER: A DECADE TO GET A DIAGNOSIS THAT FITS
    Janarthen, Vahini
    Warner, Graham
    JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 2016, 87 (12):
  • [5] Biotinidase deficiency in differential diagnosis of neuromyelitis optica spectrum disorder
    Bilge, Nuray
    Yevgi, Recep
    MULTIPLE SCLEROSIS AND RELATED DISORDERS, 2020, 44
  • [6] Evoked potentials are useful for diagnosis of neuromyelitis optica spectrum disorder
    Ohnari, Keiko
    Okada, Kazumasa
    Takahashi, Toshiyuki
    Mafune, Kosuke
    Adachi, Hiroaki
    JOURNAL OF THE NEUROLOGICAL SCIENCES, 2016, 364 : 97 - 101
  • [7] How to avoid missing a diagnosis of neuromyelitis optica spectrum disorder
    Contentti, Edgar Carnero
    Rotstein, Dalia
    Okuda, Darin T.
    Paul, Friedemann
    MULTIPLE SCLEROSIS JOURNAL, 2025, 31 (01) : 8 - 22
  • [8] Neuromyelitis optica spectrum disorder and menstruation
    Badihian, Sheruin
    Manouchehri, Navid
    Mirmosayyeb, Omid
    Ashtari, Fereshteh
    Shaygannejad, Vahid
    REVUE NEUROLOGIQUE, 2018, 174 (10) : 716 - 721
  • [9] Pediatric Neuromyelitis Optica Spectrum Disorder
    Poisson, Kelsey
    Moeller, Karen
    Fisher, Kristen S.
    SEMINARS IN PEDIATRIC NEUROLOGY, 2023, 46 : 1 - 8
  • [10] Neuromyelitis optica spectrum disorder: an overview
    Ramakrishnan, Pooja
    Nagarajan, Devipriya
    ACTA NEUROBIOLOGIAE EXPERIMENTALIS, 2020, 80 (03) : 256 - 272