A Case of Erdheim-Chester Disease Causing Secondary Sclerosing Cholangitis

被引:1
|
作者
Kamalumpundi, Vijayvardhan [1 ]
Rieth, John [2 ]
Tran, Huy [3 ]
Ashat, Munish [3 ]
Zhang, Xiaocen [3 ]
机构
[1] Univ Iowa, Roy J & Lucille A Carver Coll Med, Iowa City, IA USA
[2] Univ Iowa Hosp & Clin, Div Hematol Oncol Blood & Marrow Transplantat, Iowa City, IA USA
[3] Univ Iowa Hosp & Clin, Dept Internal Med, Div Gastroenterol & Hepatol, Iowa City, IA 52242 USA
关键词
myeloid neoplasms; histiocytosis; IgG4; disease; obstructive cholangiopathy;
D O I
10.14309/crj.0000000000000963
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
Erdheim-Chester disease (ECD) is an exceedingly rare and aggressive disease characterized by foamy CD68 + CDa-histiocytic infiltration into multiple tissues and organs. Only 1,500 cases have been diagnosed since 1930 when ECD was first described. Biliary tract involvement of ECD has only been reported in the literature once. We report a case of ECD causing extrahepatic biliary obstruction without significant bile duct dilation, mimicking primary sclerosing cholangitis or IgG4 disease.
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页数:2
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