Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare but aggressive malignancy with high mortality involving the skin and hematopoietic system. Clinical suspicion is difficult, and management of skin lesions is challenging due to their indolent course prior to dissemination. We describe a patient with isolated skin involvement who progressed to CD4+/CD56+ and CD123+ acute leukemia.
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Sichuan Univ, West China Hosp, Dept Oncol, 37 Guo Xue Xiang, Chengdu 610041, Sichuan, Peoples R ChinaSichuan Univ, West China Hosp, Dept Oncol, 37 Guo Xue Xiang, Chengdu 610041, Sichuan, Peoples R China
Yang, Chunli
Zhao, Sha
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Sichuan Univ, West China Hosp, Dept Pathol, 37 Guo Xue Xiang, Chengdu 610041, Sichuan, Peoples R ChinaSichuan Univ, West China Hosp, Dept Oncol, 37 Guo Xue Xiang, Chengdu 610041, Sichuan, Peoples R China
Zhao, Sha
Wang, Lin
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Sichuan Univ, West China Hosp, Dept Dermatol, 37 Guo Xue Xiang, Chengdu 610041, Sichuan, Peoples R ChinaSichuan Univ, West China Hosp, Dept Oncol, 37 Guo Xue Xiang, Chengdu 610041, Sichuan, Peoples R China
Wang, Lin
Zou, Liqun
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Sichuan Univ, West China Hosp, Dept Oncol, 37 Guo Xue Xiang, Chengdu 610041, Sichuan, Peoples R ChinaSichuan Univ, West China Hosp, Dept Oncol, 37 Guo Xue Xiang, Chengdu 610041, Sichuan, Peoples R China