Pharmacological Activation of CFTR Function improves Airway Epithelial Homeostasis and Immune Defense in Children with Cystic Fibrosis

被引：0

作者：

Loske, J. ^{[1
,2
]}

Voeller, M. ^{[3
]}

Lukassen, S. ^{[4
]}

Stahl, M. ^{[3
,5
,6
]}

Thuermann, L. ^{[1
]}

Seegebarth, A. ^{[1
]}

Roehmel, J. ^{[3
,5
,6
]}

Wisniewski, S. ^{[3
]}

Messingschlager, M. ^{[1
,2
]}

Lorenz, S. ^{[7
]}

Klages, S. ^{[7
]}

Eils, R. ^{[4
,6
,8
]}

Lehmann, I. ^{[1
,5
,6
]}

Mall, M. ^{[3
,5
,6
]}

Trump, S. ^{[1
]}

Graeber, S. Y. ^{[3
,5
,6
]}

机构：

[1] Berliner Inst Gesundheitsforsch Charite, Forsch Grp Mol Epidemiol, Berlin, Germany

[2] Free Univ Berlin, Inst Biol, Berlin, Germany

[3] Charite, Klin Padiatr Pneumol Immunol & Intensivmed, Berlin, Germany

[4] Berliner Inst Gesundheitsforsch Charite, Ctr Digital Hlth, Berlin, Germany

[5] Berliner Inst Gesundheitsforsch Charite, Berlin, Germany

[6] Deutsch Zentrum Lungenforsch DZL, Assoziertes Zentrum, Berlin, Germany

[7] Max Planck Inst Mol Genet, Berlin, Germany

[8] Univ Klinikum Heidelberg, Hlth Data Sci Unit, Heidelberg, Germany

来源：

KLINISCHE PADIATRIE | 2024年 / 236卷 / 02期

关键词：

D O I：

10.1055/s-0044-1779396

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

0050

引用

页码：S23 / S23

页数：1

共 50 条

[1] Pharmacological Improvement of Cystic Fibrosis Transmembrane Conductance Regulator Function Rescues Airway Epithelial Homeostasis and Host Defense in Children with Cystic Fibrosis
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