Chordoma in children: Case-report and review of literature

被引:10
|
作者
Habrand, Jean-Louis [1 ,2 ,3 ]
Datchary, Jean [1 ,2 ,3 ]
Bolle, Stephanie [3 ]
Beaudre, Anne [3 ]
de Marzi, Ludovic [2 ]
Beccaria, Kevin [4 ]
Stefan, Dinu [1 ]
Grill, Jacques [5 ]
Dendale, Remi [2 ]
机构
[1] Ctr Francois Baclesse, Dept Radiat Oncol, 3 Rue Gen Harris, F-14076 Caen, France
[2] Inst Curie, Dept Radiat Oncol, Protontherapy Ctr, Campus Univ, F-91406 Orsay, France
[3] Gustave Roussy Canc Campus, Dept Radiat Oncol, 114 Rue Edouard Vaillant, F-94805 Villejuif, France
[4] Ctr Hosp Necker Enfants Malad, Dept Pediat Neurosurg, 149 Rue Sevres, F-75015 Paris, France
[5] Gustave Roussy Canc Campus, Dept Pediat Oncol, 144 Rue Edouard Vaillant, F-94805 Villejuif, France
关键词
Chordoma; Sarcoma; Protontherapy; Childrena;
D O I
10.1016/j.rpor.2015.10.007
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
We report an exceptional case of a very late local failure in a 9-year-old boy presenting with a chordoma of the cranio-cervical junction. The child was initially treated with a combination of surgical resection followed by high dose photon-proton radiation therapy. This aggressive therapy allowed a 9-year remission with minimal side-effects. Unfortunately, he subsequently presented with a local failure managed with a second full-dose course of protons. The child died one year later from local bleeding of unclear etiology. (C) 2015 Greater Poland Cancer Centre. Published by Elsevier Sp. z o.o. All rights reserved.
引用
收藏
页码:1 / 7
页数:7
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