RESTING METABOLIC-RATE IN HOMOZYGOUS SICKLE-CELL DISEASE

被引:66
|
作者
SINGHAL, A [1 ]
DAVIES, P [1 ]
SAHOTA, A [1 ]
THOMAS, PW [1 ]
SERJEANT, GR [1 ]
机构
[1] UNIV CAMBRIDGE,DUNN NUTR UNIT,CAMBRIDGE,ENGLAND
来源
关键词
ANEMIA; SICKLE CELL; ENERGY EXPENDITURE; BASAL METABOLISM;
D O I
10.1093/ajcn/57.1.32
中图分类号
R15 [营养卫生、食品卫生]; TS201 [基础科学];
学科分类号
100403 ;
摘要
The resting metabolic rate in 20 patients with homozygous sickle cell (SS) disease was 19% higher than in 20 age- and sex-matched control subjects with a normal hemoglobin genotype (AA). The difference was not accounted for by differences in lean body mass. It is postulated that this increased energy expenditure reflects the energy expenditure of erythropoietic hyperplasia and leads to a marginal nutritional state that may contribute to the abnormal growth in SS disease.
引用
收藏
页码:32 / 34
页数:3
相关论文
共 50 条
  • [1] RESTING METABOLIC-RATE IN SICKLE-CELL DISEASE - REPLY
    SINGHAL, A
    THOMAS, P
    SERJEANT, GR
    [J]. AMERICAN JOURNAL OF CLINICAL NUTRITION, 1993, 58 (05): : 710 - 711
  • [2] WHOLE-BODY PROTEIN-TURNOVER AND RESTING METABOLIC-RATE IN HOMOZYGOUS SICKLE-CELL DISEASE
    BADALOO, A
    JACKSON, AA
    JAHOOR, F
    [J]. CLINICAL SCIENCE, 1989, 77 (01) : 93 - 97
  • [3] Energy intake and resting metabolic rate in preschool Jamaican children with homozygous sickle cell disease
    Singhal, A
    Parker, S
    Linsell, L
    Serjeant, G
    [J]. AMERICAN JOURNAL OF CLINICAL NUTRITION, 2002, 75 (06): : 1093 - 1097
  • [4] HOMOZYGOUS SICKLE-CELL DISEASE IN JAMAICA
    ENNIS, JT
    SERJEANT, GR
    MIDDLEMISS, H
    [J]. BRITISH JOURNAL OF RADIOLOGY, 1973, 46 (551): : 943 - 950
  • [5] PRIAPISM AND IMPOTENCE IN HOMOZYGOUS SICKLE-CELL DISEASE
    EMOND, AM
    HOLMAN, R
    HAYES, RJ
    SERJEANT, GR
    [J]. ARCHIVES OF INTERNAL MEDICINE, 1980, 140 (11) : 1434 - 1437
  • [6] ANTIPHOSPHOLIPID ANTIBODIES IN HOMOZYGOUS SICKLE-CELL DISEASE
    DECEULAER, K
    KHAMASHTA, MA
    HARRIS, EN
    SERJEANT, GR
    HUGHES, GRV
    [J]. ANNALS OF THE RHEUMATIC DISEASES, 1992, 51 (05) : 671 - 672
  • [7] ABDOMINAL COMPLICATIONS IN HOMOZYGOUS SICKLE-CELL DISEASE
    MCCALL, IW
    [J]. BRITISH JOURNAL OF RADIOLOGY, 1978, 51 (601): : 71 - 72
  • [8] DELAYED MENARCHE IN HOMOZYGOUS SICKLE-CELL DISEASE
    GRAHAM, C
    MAUDE, GH
    SERJEANT, GR
    [J]. WEST INDIAN MEDICAL JOURNAL, 1986, 35 (01): : 18 - 22
  • [9] CLINICAL PRESENTATION OF HOMOZYGOUS SICKLE-CELL DISEASE
    BAINBRIDGE, R
    HIGGS, DR
    MAUDE, GH
    SERJEANT, GR
    [J]. JOURNAL OF PEDIATRICS, 1985, 106 (06): : 881 - 885
  • [10] THE DEVELOPMENT OF CARDIOMEGALY IN HOMOZYGOUS SICKLE-CELL DISEASE
    STEVENS, MCG
    CROOKS, GW
    SERJEANT, GR
    [J]. WEST INDIAN MEDICAL JOURNAL, 1985, 34 (04): : 253 - 256