PRENATAL-DIAGNOSIS OF A GIANT INTRACRANIAL TERATOMA ASSOCIATED WITH PULMONARY HYPOPLASIA

被引:23
|
作者
WEYERTS, LK
CATANZARITE, V
JONES, MC
MENDOZA, A
机构
[1] SHARP MEM HOSP & REHABIL CTR,MARY BIRCH HOSP WOMEN,SAN DIEGO,CA
[2] CHILDRENS HOSP SAN DIEGO,DIV DYSMORPHOL,SAN DIEGO,CA
关键词
D O I
10.1136/jmg.30.10.880
中图分类号
Q3 [遗传学];
学科分类号
071007 ; 090102 ;
摘要
We present a case in which an intracranial tumour replacing all intracranial contents was diagnosed by sonography at 31 weeks' gestation. The patient was delivered by caesarean section and died shortly after delivery. At necropsy, the tumour was found to be a teratoma with no recognisable normal brain tissue present. Additional findings at necropsy included pulmonary and adrenal hypoplasia. The diagnosis and prognosis of intracranial teratomas diagnosed in utero, and the association of this tumour with pulmonary hypoplasia, are discussed.
引用
收藏
页码:880 / 882
页数:3
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