ORAL COMPLICATIONS IN TYPE-1B GLYCOGEN-STORAGE DISEASE

被引:12
|
作者
BARRETT, AP [1 ]
BUCKLEY, DJ [1 ]
KATELARIS, CH [1 ]
机构
[1] WESTMEAD HOSP,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
关键词
D O I
10.1016/0030-4220(90)90323-K
中图分类号
R78 [口腔科学];
学科分类号
1003 ;
摘要
A case of type 1b glycogen storage disease (GSD) in which neutropenia and neutrophil dysfunction were prominent features is described. Oral complications included rapidly progressive periodontal disease and recurrent mucosal ulceration. © 1990.
引用
收藏
页码:174 / 176
页数:3
相关论文
共 50 条
  • [1] BIOCHEMICAL-DIAGNOSIS OF TYPE-1B GLYCOGEN-STORAGE DISEASE
    HAWKINS, RA
    KAMATH, KR
    DORNEY, SFA
    ADAMS, A
    AUSTRALIAN PAEDIATRIC JOURNAL, 1984, 20 (03): : 217 - 220
  • [2] GLYCOGEN-STORAGE DISEASES TYPE-1B AND TYPE-1C
    DEPARSCAU, L
    GUIBAUD, P
    MAIRE, I
    PEDIATRIE, 1988, 43 (08): : 661 - 665
  • [3] ACUTE MYELOGENOUS LEUKEMIA AND MALIGNANT HYPERTHERMIA IN A PATIENT WITH TYPE-1B GLYCOGEN-STORAGE DISEASE
    SIMMONS, PS
    SMITHSON, WA
    GRONERT, GA
    HAYMOND, MW
    JOURNAL OF PEDIATRICS, 1984, 105 (03): : 428 - 431
  • [4] A DIRECT METHOD FOR THE DIAGNOSIS OF HUMAN HEPATIC TYPE-1B AND TYPE-1C GLYCOGEN-STORAGE DISEASE
    WADDELL, ID
    HUME, R
    BURCHELL, A
    CLINICAL SCIENCE, 1989, 76 (06) : 573 - 579
  • [5] GLYCOGEN-STORAGE DISEASE TYPE-1B DUE TO A DEFECT OF GLUCOSE-6-PHOSPHATE TRANSLOCASE
    NARISAWA, K
    OTOMO, H
    IGARASHI, Y
    ARAI, N
    OTAKE, M
    TADA, K
    KUZUYA, T
    JOURNAL OF INHERITED METABOLIC DISEASE, 1982, 5 (04) : 227 - 228
  • [6] LITHIUM-CARBONATE (LI) THERAPY FOR NEUTROPENIA OF GLYCOGEN-STORAGE DISEASE (GSD) TYPE-1B
    MAHONEY, DH
    ANDERSON, DC
    BEAUDET, AL
    CLINICAL RESEARCH, 1981, 29 (05): : A885 - A885
  • [7] GLYCOGEN-STORAGE DISEASE TYPE-1B - GENETIC DISORDER INVOLVING THE TRANSPORT-SYSTEM OF INTRACELLULAR MEMBRANE
    NARISAWA, K
    IGARASHI, Y
    TADA, K
    ENZYME, 1987, 38 (1-4) : 177 - 183
  • [8] HYPERURICEMIA IN GLYCOGEN-STORAGE DISEASE TYPE 1
    FINE, RN
    STRAUSS, J
    DONNELL, GN
    AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1966, 112 (06): : 572 - &
  • [9] DIAGNOSIS OF TYPE-1B AND TYPE-1C GLYCOGEN-STORAGE-DISEASE
    BURCHELL, A
    GIBB, L
    JOURNAL OF INHERITED METABOLIC DISEASE, 1991, 14 (03) : 305 - 307
  • [10] BRAIN ABSCESSES IN GLYCOGEN-STORAGE DISEASE-TYPE-1B
    GARTY, BZ
    RACHMEL, A
    MANDEL, H
    NITZAN, M
    ACTA PAEDIATRICA, 1992, 81 (11) : 948 - 948