A Case With Dextrocardia and Multiple Cardiac Anomalies in a Family With Congenital Heart Malformations

In this case; an interesting example of family with recurrent congenital heart defects due to situs ambiguous has been presented. The parents were relatives and had a history of termination because of complex congenital cardiac malformations in the first pregnancy. Dextrocardia and complex malformations of the heart and great vessels were detected in the second pregnacy by fetal echocardiography at 23rd weeks of gestation. Postmortem evaluation confirmed prenatal findings on fetal echocardiography and also revealed medially placed liver, dextrocardia and a spleen on normal location. We suggest that all cases with complex congenital malformations of heart and/or great vessels must be assessed for the heterotaxy disorders because of the findings in this family.