AUTOSOMAL-DOMINANT POLYCYSTIC KIDNEY-DISEASE

被引:806
|
作者
GABOW, PA
机构
[1] Department of Medicine, University of Colorado Health Sciences Center, Denver, CO 80262, Box C-283
来源
NEW ENGLAND JOURNAL OF MEDICINE | 1993年 / 329卷 / 05期
关键词
D O I
10.1056/NEJM199307293290508
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Autosomal dominant polycystic kidney disease is one of the most common hereditary disorders, being 10 times more common than sickle cell disease, 15 times more common than cystic fibrosis, and 20 times more common than Huntington's disease. In addition, the disease accounts for 8 to 10 percent of the cases of end-stage renal disease, for which medical care costs exceed $200 million a year. The name previously given to the disorder, “adult polycystic kidney disease,” belies its true scope by focusing on the kidney and by confining the disorder to adults. In fact, autosomal dominant polycystic kidney disease is a… © 1993, Massachusetts Medical Society. All rights reserved.
引用
收藏
页码:332 / 342
页数:11
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