SPLENIC SEQUESTRATION AND INEFFECTIVE ERYTHROPOIESIS IN HEMOGLOBIN-E-BETA-THALASSEMIA DISEASE

被引:10
|
作者
RUYMANN, FB [1 ]
POPEJOY, LA [1 ]
BROUILLARD, RB [1 ]
机构
[1] UNIFORMED SERV UNIV HLTH SCI,WALTER REED ARMY MED CTR,SCH MED,DEPT MED,WASHINGTON,DC
关键词
D O I
10.1203/00006450-197810000-00014
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:1020 / 1023
页数:4
相关论文
共 50 条
  • [1] INEFFECTIVE ERYTHROPOIESIS IN HEMOGLOBIN E-BETA-THALASSEMIA - AN ELECTRON-MICROSCOPE STUDY
    WICKRAMASINGHE, SN
    HUGHES, M
    WASI, P
    FUCHAROEN, S
    MODELL, B
    BRITISH JOURNAL OF HAEMATOLOGY, 1981, 48 (03) : 451 - &
  • [2] STUDY OF A HEMOGLOBIN-E-BETA-THALASSEMIA ASSOCIATION IN A SUBJECT OF SYRIAN DESCENT
    VIDAUD, M
    SCHAISON, G
    LEVERGER, G
    NOUVELLE REVUE FRANCAISE D HEMATOLOGIE, 1986, 28 (03): : 178 - 178
  • [3] A mechanism of ineffective erythropoiesis in β-thalassemia/Hb E disease
    Lithanatudom, Pathrapol
    Leecharoenkiat, Amporn
    Wannatung, Tirawat
    Svasti, Saovaros
    Fucharoen, Suthat
    Smith, Duncan R.
    HAEMATOLOGICA-THE HEMATOLOGY JOURNAL, 2010, 95 (05): : 716 - 723
  • [4] Hydroxyurea increases hemoglobin F levels and improves the effectiveness of erythropoiesis in beta-thalassemia hemoglobin E disease
    Fucharoen, S
    Siritanaratkul, N
    Winichagoon, P
    Chowthaworn, J
    Siriboon, W
    Muangsup, W
    Chaicharoen, S
    Poolsup, N
    Chindavijak, B
    Pootrakul, P
    Piankijagum, A
    Schechter, AN
    Rodgers, GP
    BLOOD, 1996, 87 (03) : 887 - 892
  • [5] Hepcidin is suppressed by erythropoiesis in hemoglobin E β-thalassemia and β-thalassemia trait
    Jones, Emma
    Pasricha, Sant-Rayn
    Allen, Angela
    Evans, Patricia
    Fisher, Chris A.
    Wray, Katherine
    Premawardhena, Anuja
    Bandara, Dyananda
    Perera, Ashok
    Webster, Craig
    Sturges, Pamela
    Olivieri, Nancy F.
    St Pierre, Timothy
    Armitage, Andrew E.
    Porter, John B.
    Weatherall, David J.
    Drakesmith, Hal
    BLOOD, 2015, 125 (05) : 873 - 880
  • [6] BETA-THALASSEMIA HEMOGLOBIN E DISEASE IN VIETNAM
    KHANH, NG
    THU, LT
    TRUC, DB
    HOA, DP
    HOA, TT
    HA, TH
    AMERICAN JOURNAL OF HUMAN GENETICS, 1991, 49 (04) : 153 - 153
  • [8] BETA-THALASSEMIA HEMOGLOBIN-E DISEASE IN VIETNAM
    KHANH, NC
    THU, LT
    TRUC, DB
    HOA, DP
    HOA, TT
    HA, TH
    JOURNAL OF TROPICAL PEDIATRICS, 1990, 36 (01) : 43 - 45
  • [9] FERROPORTIN INHIBITORS IMPROVE INEFFECTIVE ERYTHROPOIESIS AND PREVENT IRON LOADING IN A BETA-THALASSEMIA DISEASE MODEL
    Manolova, Vania
    Flace, Anna
    Altermatt, Patrick
    Sundstrom, Hanna
    Nyffenegger, Naja
    Duerrenberger, Franz
    AMERICAN JOURNAL OF HEMATOLOGY, 2017, 92 (08) : E224 - E224
  • [10] Fetal hemoglobin rescues ineffective erythropoiesis in sickle cell disease
    El Hoss, Sara
    Cochet, Sylvie
    Godard, Auria
    Yan, Hongxia
    Dussiot, Michael
    Frati, Giacomo
    Boutonnat-Faucher, Benedicte
    Laurance, Sandrine
    Renaud, Olivier
    Joseph, Laure
    Miccio, Annarita
    Brousse, Valentine
    Mohandas, Narla
    El Nemer, Wassim
    HAEMATOLOGICA, 2021, 106 (10) : 2707 - 2719