CLOUSTON SYNDROME - A RARE AUTOSOMAL DOMINANT TRAIT WITH PALMOPLANTAR HYPERKERATOSIS AND ALOPECIA

被引:0
|
作者
PATEL, RRA
BIXLER, D
NORINS, AL
机构
[1] INDIANA UNIV,SCH DENT,DEPT MED GENET,INDIANAPOLIS,IN 46202
[2] INDIANA UNIV,SCH DENT,DEPT DERMATOL,INDIANAPOLIS,IN 46202
来源
JOURNAL OF CRANIOFACIAL GENETICS AND DEVELOPMENTAL BIOLOGY | 1991年 / 11卷 / 03期
关键词
ECTODERMAL DYSPLASIA; ALOPECIA; PALMAR AND PLANTAR HYPERKERATOSIS; ABNORMAL HAIR; DYSPLASTIC NAILS;
D O I
暂无
中图分类号
R602 [外科病理学、解剖学]; R32 [人体形态学];
学科分类号
100101 ;
摘要
A caucasian family is reported in which four males and four females in two generations have exhibited alopecia, dysplastic nails, and hyperkeratosis of palmar and plantar surfaces. This type of ectodermal dysplasia, Clouston syndrome, features normal teeth with severe hair and nail dysplasia.
引用
收藏
页码:176 / 179
页数:4
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