ANGIOTROPIC LYMPHOMA (MALIGNANT ANGIOENDOTHELIOMATOSIS) PRESENTING WITH RAPIDLY PROGRESSIVE DEMENTIA

被引:15
|
作者
DRLICEK, M
GRISOLD, W
LISZKA, U
HITZENBERGER, P
MACHACEK, E
机构
[1] LUDWIG BOLTZMANN INST KLIN NEUROBIOL,A-1145 VIENNA,AUSTRIA
[2] KAISER FRANZ JOSEF SPITAL,NEUROL ABT,A-1100 VIENNA,AUSTRIA
[3] KAISER FRANZ JOSEF SPITAL,INST PATHOL BAKTERIOL,A-1100 VIENNA,AUSTRIA
关键词
ANGIOTROPIC LYMPHOMA; CREUTZFELDT-JAKOB DISEASE; DEMENTIA; MALIGNANT ANGIOENDOTHELIOMATOSIS;
D O I
10.1007/BF00293391
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
An 87-year-old male presented with rapidly progressive dementia, disorder of consciousness and myoclonus, suggesting Creutzfeldt-Jakob disease, but with nonspecific EEG and negative CT findings. Autopsy revealed a malignant angiotropic lymphoma with accumulation of tumor cells within small vessels of the brain and visceral organs. Immunohistochemistry disclosed a large cell lymphoma of B cell type.
引用
收藏
页码:533 / 535
页数:3
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