TYPE-III HYPERLIPOPROTEINEMIA IN A CHILD WITH HEMOLYTIC UREMIC SYNDROME

被引:9
|
作者
FEUSSNER, G [1 ]
WINGEN, AM [1 ]
ZIEGLER, R [1 ]
机构
[1] UNIV HEIDELBERG,DEPT PEDIAT,W-6900 HEIDELBERG,GERMANY
来源
METABOLISM-CLINICAL AND EXPERIMENTAL | 1990年 / 39卷 / 11期
关键词
D O I
10.1016/0026-0495(90)90094-S
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
The case of a 6-year-old girl with severe hyperlipoproteinemia and chronic renal failure that developed after hemolytic uremic syndrome (HUS) is reported. The patient was homozygous for apolipoprotein (apo) E2, and her very-low-density lipoprotein (VLDL)-cholesterol/serum-triglyceride (TG) ratio of 0.63 was unusually high. She was consistently diagnosed to have type III hyperlipoproteinemia (HLP). This is the first report of type III HLP in a child with chronic renal disease. © 1990.
引用
收藏
页码:1196 / 1199
页数:4
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