MOLECULAR-BASIS OF PYRUVATE-KINASE DEFICIENCY .2. ROLE OF THIOL-GROUPS IN PYRUVATE-KINASE FROM PYRUVATE KINASE-DEFICIENT PATIENTS

被引:31
|
作者
VANBERKEL, TJ
STAAL, GEJ
KOSTER, JF
NYESSEN, JG
机构
[1] ERASMUS UNIV, FAC MED, DEPT BIOCHEM 1, ROTTERDAM, NETHERLANDS
[2] STATE UNIV UTRECHT HOSP, HAEMATOL DEPT, UTRECHT, NETHERLANDS
关键词
D O I
10.1016/0005-2744(74)90179-X
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:361 / 367
页数:7
相关论文
共 50 条
  • [1] MOLECULAR-BASIS OF PYRUVATE-KINASE DEFICIENCY
    BLUME, KG
    ARNOLD, H
    LOHR, GW
    SCHOLZ, G
    BIOCHIMICA ET BIOPHYSICA ACTA, 1974, 370 (02) : 601 - 604
  • [2] THE MOLECULAR-BASIS OF CANINE PYRUVATE-KINASE DEFICIENCY
    WHITNEY, KM
    GOODMAN, SA
    BAILEY, EM
    LOTHROP, CD
    EXPERIMENTAL HEMATOLOGY, 1994, 22 (09) : 866 - 874
  • [3] FUNCTION OF THIOL-GROUPS IN YEAST PYRUVATE-KINASE
    WIEKER, HJ
    HESS, B
    HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE, 1972, 353 (12): : 1877 - 1893
  • [4] PYRUVATE-KINASE ELECTROPHORESIS IN NORMAL AND PYRUVATE-KINASE DEFICIENT HEMOLYSATES
    WONNEBERGER, B
    SCHROTER, W
    CLINICA CHIMICA ACTA, 1974, 51 (02) : 147 - 150
  • [5] MONOMERIC FORM OF PYRUVATE-KINASE IN HUMAN PYRUVATE-KINASE DEFICIENCY
    ADACHI, K
    GHORY, PK
    ASAKURA, T
    SCHWARTZ, E
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1977, 74 (02) : 501 - 504
  • [6] PYRUVATE-KINASE DEFICIENCY
    MIWA, S
    FUJII, H
    CLINICAL BIOCHEMISTRY, 1990, 23 (02) : 155 - 157
  • [7] PYRUVATE-KINASE DEFICIENCY
    MIWA, S
    ACTA HAEMATOLOGICA JAPONICA, 1987, 50 (08): : 1445 - 1452
  • [8] ROLE OF THIOL-GROUPS IN NORMAL AND ABNORMAL PYRUVATE-KINASE FROM HUMAN ERYTHROCYTES
    VANBERKE.TJ
    STALL, GEJ
    KOSTER, JF
    EUROPEAN JOURNAL OF CLINICAL INVESTIGATION, 1974, 4 (05) : 331 - 331
  • [9] RESEARCH ON MEMBRANE-LOCALIZED ERYTHROCYTIC PYRUVATE-KINASE IN PATIENTS WITH PYRUVATE-KINASE DEFICIENCY
    LAKOMEK, M
    WINKLER, H
    TILLMANN, W
    SCHROTER, W
    BLUT, 1980, 41 (04): : 285 - 285
  • [10] FUNCTION OF THIOL GROUPS OF PYRUVATE-KINASE FROM YEAST
    WIEKER, HJ
    HESS, B
    HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE, 1972, 353 (05): : 769 - &