RECURRENT PERITONITIS IN A PATIENT WITH FAMILIAL MEDITERRANEAN FEVER

被引:0
|
作者
DHONDT, A [1 ]
DEPOTTER, W [1 ]
MAST, A [1 ]
VANMAELE, V [1 ]
机构
[1] ALGEMENE KLIN HEILIGE FAMILIE,DEPT GASTROENTEROL,GROENEBRIEL 1,B-9000 GHENT,BELGIUM
来源
ACTA GASTRO-ENTEROLOGICA BELGICA | 1991年 / 54卷 / 02期
关键词
PERIODIC DISEASE; FAMILIAL MEDITERRANEAN FEVER; DOPAMINE BETA-HYDROXYLASE; PERITONITIS;
D O I
暂无
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
The authors report a case of Familial Mediterranean Fever (FMF) in a Turkish patient. FMF is characterised by paroxysmal attacks of fever, peritonitis and/or pleuritis or arthritis. FMF is almost exclusively confined to populations of Mediterranean origin and it is often familial. The diagnosis is mainly clinical. Recently an enhanced dopamine beta-hydroxylase (DBH) activity was described as a diagnostic test. We confirmed this in our patient. FMF was successfully treated by chronic colchicine therapy: 1-2 mg daily, which reduced DBH activity to normal levels.
引用
收藏
页码:209 / 213
页数:5
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